Oncogenic osteomalacia associated with an occult phosphaturic mesenchymal tumour: clinico-radiologico-pathological correlation and ultrastructural studies.
نویسندگان
چکیده
A middle-aged man presented with bone pain at multiple sites due to tumour-induced osteomalacia. The underlying occult phosphaturic mesenchymal tumour was identified by octreotide scan 5 years after presentation and confirmed by computed tomography. Tumour resection resulted in normalisation of blood chemistry and bone densitometry. Clinico-radiologico-pathological correlation and ultrastructural studies of the tumour threw light on the pathogenesis and pathophysiology of this rare disease.
منابع مشابه
Expectations of response from octreotide therapy in recurrent phosphaturic mesenchymal tumors--do they reflect reality?
Phosphaturic mesenchymal tumor (PMT) is a rare and small tumor leading to oncogenic osteomalacia and deriving mostly from benign mesenchymal origin. The tumor may originate in any part of the body such as soft tissue or bone site, but is more frequent in the upper and lower extremities and craniofacial sinuses. Its most common type is oncogenic osteomalacia (OO) associated phosphaturic mesenchy...
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ورودعنوان ژورنال:
- Hong Kong medical journal = Xianggang yi xue za zhi
دوره 12 4 شماره
صفحات -
تاریخ انتشار 2006